Syngnathia Without Any Other Associated Anomaly: A Very Rare Case Report

Congenital fusion of the mandible to maxilla is a rare phenomenon. The fusion can be a bony fusion in which case it's referred to as Syngnathia or soft tissue fusion when it's addressed as Synechiae. [1] Soft tissues fusion is involved most often in the oral cavity but it may involve both hard and soft tissues of the child. This results in inability of child to thrive as it doesn't allow mouth opening and feeding. This is a case report of a 3-day-old baby boy with partial maxilla-mandibular fusion from right canine to posterior jaw who was brought to Oral and Maxillofacial department of the dental centre in GMC Hospital, Ajman, UAE for treatment because of inability to thrive.

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Synechiae of the Oral Cavity with Cleft Palate: A Rare Congenital Anomaly

Kumar¹,

Singh²,

Rautela³

et al. 2018

International Journal of Head and Neck Surgery

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Aim: Fusion defects of maxilla and mandible are a rare congenital anomaly that affect the growth and development of patients in varying extents. Authors intend to present a case of incomplete synechiae of the oral cavity. Background: Congenital maxillo-mandibular fusions present with varying degree of involvement of mucosa, soft tissues and bone and can cause aerodigestive problems in the neonatal period. Case description: A 5-day-old male child was referred from pediatrics for evaluation for complaints of inability to feed. On examination, a mucosal band was noted connecting the floor of the mouth with the hard palate, with free margins on both sides. After proper consent, the mucosal band was completely excised under local anesthesia and hemostasis was achieved. The rest of the oral cavity and oropharynx was normal except cleft palate. Conclusion: These types of anomalies have to be diagnosed as early as possible in the early neonatal life. Early diagnosis and appropriate management should be instituted to prevent risks of asphyxia, aspiration pneumonitis, growth retardation, malnutrition, facial growth abnormalities, and improper eruption of teeth. Clinical significance: As there are various types of presentations, the treatment needs to be individualized.

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Syngnathia Without Any Other Associated Anomaly: A Very Rare Case Report

Cited by 3 publications

References 14 publications

Congenital Fibrous Maxillomandibular Fusion

Congenital Fibrous Maxillomandibular Fusion

Congenital Fusion of the Mandible and Maxilla- A Case Report from Ajman, United Arab Emirates

Synechiae of the Oral Cavity with Cleft Palate: A Rare Congenital Anomaly

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