Tetralogy of Fallot with a Single Pulmonary Artery: Operative Repair

Mistrot, J. Jacques; Bernhard, William F.; Rosenthal, Amnon; Castañeda, Aldo R.

doi:10.1016/s0003-4975(10)64118-5

Cited by 26 publications

(10 citation statements)

References 8 publications

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“…There are multiple reports of successful “single-lung” intracardiac repair for congenital absence of one pulmonary artery. 5 -7 However, our case appears to be one where “single pulmonary artery” was an acquired condition.…”

Section: Discussionmentioning

confidence: 72%

“…The mortality for single-lung intracardiac repair of TOF was reported to be as high as 48% in some earlier studies and ranges from 5% to 8.3% in some more recent ones. 6,7 There are very few long-term studies. 6 The overall outcome is generally favorable, although there are reports of occasional complications such as hemoptysis from the contralateral lung, necessitating coil embolization of the culprit vessel.…”

Section: Discussionmentioning

confidence: 99%

See 1 more Smart Citation

One-Stage Repair of Tetralogy of Fallot and Pseudoaneurysm of the Ascending Aorta After Central Shunt

Katewa

Anand

Sahu

2018

World J Pediatr Congenit Heart Surg

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Pseudoaneurysm of the ascending aorta following a central aortopulmonary shunt is a rare and potentially fatal complication. Loss of pulmonary artery continuity is another complication following an aortopulmonary shunt. We report an unusual combination of these two complications following an aortopulmonary shunt performed in a child with tetralogy of Fallot. This was managed successfully along with intracardiac repair of tetralogy of Fallot incorporating only the left pulmonary artery.

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Section: Discussionmentioning

confidence: 72%

Section: Discussionmentioning

confidence: 99%

One-Stage Repair of Tetralogy of Fallot and Pseudoaneurysm of the Ascending Aorta After Central Shunt

Katewa

Anand

Sahu

2018

World J Pediatr Congenit Heart Surg

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“…The rst successful complete repair of this defect was published by Sherrick [24] and the operative mortality in the past was 44% to 48%. [25] Numerous studies have reported the repair of this defect without revascularization of the affected lung.…”

Section: Discussionmentioning

confidence: 99%

Early Single-Stage Surgical Revascularization of Pulmonary Artery in Unilateral Absence of a Pulmonary Artery

Xia

et al. 2020

Preprint

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BackgroundThis research aims to summarize the findings of the early single-stage revascularization of remnant pulmonary artery in unilateral absent intrapericardial pulmonary artery. MethodsWe retrospectively analyzed the medical records of 10 patients with unilateral absent pulmonary artery, in which 7 were right and 3 were left, the median age and median weight at surgery was 4 months and 5.2 kg, respectively. The patients received operation from January 2009 to June 2020. ResultsTen patients, 1 case associated with atrial septal defect, 2 cases with tetralogy of Fallot, and 1 case with aortopulmonary window. The median diameter of the affected hilar pulmonary artery remnants was 3.1mm (1.6-5mm), and the Z value was -3.66±1.86 (range, -6.7 to -1.75). All the patients received single-stage revascularization: tube graft interposition in 3 patients, autologous pericardial roll in 4, direct anastomosis in one, and main pulmonary artery flap angioplasty in the rest 3. No hospital deaths occurred. The follow-up period was 1 month to 5.6 years. One case underwent percutaneous balloon dilatation due to new pulmonary artery stenosis. Nonetheless, the results were encouraging, symptoms have improved in all patients. The Z value of the latest ipsilateral pulmonary artery diameter was -2.34±1.18 (range, -4.52 to -1.35), a significantly improvement when compared to the preoperative value.ConclusionsSingle-stage pulmonary artery revascularization is effective at restoring normal antegrade flow to the affected lung, resulting in improved diameter of the PA, and patient’s symptoms. However, transcatheter intervention may diminish the new pulmonary artery stenosis temporarily, reoperation is still needed in the long-term follow-up.

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“…It has been suggested that a premature closure of the ductus arteriosus may be responsible for the lack of development of the left pulmonary artery. 3 The most frequent modality of repair of TOF-ALPA reported in the literature is the so-called single lung repair or “one lung repair.” However, only few studies have been published reporting very long-term outcomes after this surgical approach.…”

Section: Introductionmentioning

confidence: 99%

Outcome at 26 Years After Repair of Fallot’s Tetralogy With Absent Left Pulmonary Artery

Stefanelli

Meli

Nardelli

et al. 2020

World J Pediatr Congenit Heart Surg

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We report long-term outcome after two-stage, “one lung repair” in a four-year-old boy with tetralogy of Fallot and congenital absence of the left pulmonary artery. The operation was carried out two years after a palliative aortopulmonary central shunt and was uneventful. Twenty-six years later, the patient is in excellent clinical condition, with normal peripheral oxygen saturation. A recent radionuclide lung scan and cardiac magnetic resonance imaging show the pulmonary flow entirely directed into the right lung. In selected cases, the long-term prognosis of patients with tetralogy of Fallot and true absence of left pulmonary artery after “one lung repair” may be excellent.

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Tetralogy of Fallot with a Single Pulmonary Artery: Operative Repair

Cited by 26 publications

References 8 publications

One-Stage Repair of Tetralogy of Fallot and Pseudoaneurysm of the Ascending Aorta After Central Shunt

One-Stage Repair of Tetralogy of Fallot and Pseudoaneurysm of the Ascending Aorta After Central Shunt

Early Single-Stage Surgical Revascularization of Pulmonary Artery in Unilateral Absence of a Pulmonary Artery

Outcome at 26 Years After Repair of Fallot’s Tetralogy With Absent Left Pulmonary Artery

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