The Vanishing Lungs!

Mohammad, Khalid; Siddiqui, Mohammad; Badireddi, Sridhar

doi:10.1164/rccm.201209-1713im

Cited by 2 publications

(3 citation statements)

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“…It usually affects young men, but it can occur in both sexes. Patients may present with a variety of symptoms, such as cough, chest pain, dyspnea and others (Tsao et al, 2012;Mohammad et al, 2013;Im et al, 2016).…”

Section: Resultsmentioning

confidence: 99%

“…It is considered a rare condition, in which pulmonary emphysema is usually observed, especially in the upper lobes, occupying more than one-third of one or both pulmonary fields. Its pathophysiology is still not completely understood, but it is known that alveolar wall destruction occurs and, consequently, it results in the formation of subpleural bullae, which agglutinate to form a giant bulla (Shah et al, 2007;Mohammad et al, 2013;Gao et al, 2015). This condition is often underdiagnosed or mistaken by pneumothorax, making it essential to perform an adequate anamnesis, associated with the indicative radiological exams (MacDuff et al, 2010;Lai et al, 2013).…”

Section: Introductionmentioning

confidence: 99%

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Vanishing lung syndrome in a pregnant woman: case report and literature review

Paiva

Simões

Lima

et al. 2022

RSD

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The presence of an underlying lung disease in pregnant women can present as a challenging case. The Vanishing Lung Syndrome is considered a rare condition, in which pulmonary emphysema is usually observed. We describe a unique case of Vanishing Lung Syndrome in pregnant patient. Female patient, 29 years old, started having progressive dyspnea on exertion in 2019, without other associated symptoms. She was hospitalized and a chest imaging study showed the presence of a large bulla in the upper right hemithorax with “hypertensive” behavior. The patient was lost to follow-up and returned two years later, pregnant, with a gestational age of 17 weeks, with an important restrictive component described in the spirometry. A bullectomy and right middle lobectomy were performed, and the patient showed significant symptom and pulmonary evaluation improvement. There are no documented cases of this rare condition in a pregnant patient, with an emphasis on seeking to maintain maternal and fetal well-being. The management of Vanishing Lung Syndrome in pregnant women is challenging, especially when lung function is impaired, as in the described case.

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Section: Resultsmentioning

confidence: 99%

Section: Introductionmentioning

confidence: 99%

Vanishing lung syndrome in a pregnant woman: case report and literature review

Paiva

Simões

Lima

et al. 2022

RSD

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“…The radiological criteria for vanishing lung syndrome includes the presence of giant bullae in one or both of the upper lobes of the lung, occupying at least one-third of the hemithorax and compressing the surrounding normal lung tissue (2). There have been numerous reports of vanishing lung syndrome (3)(4)(5)(6)(7), however there are currently no case reports of vanishing lung syndrome within one family. In the present study, five patients with vanishing lung syndrome within one family, were reported and followed up for ~20 years.…”

Section: Introductionmentioning

confidence: 99%

Vanishing lung syndrome in one family: Five cases with a 20-year follow-up

Gao

Wang

Gou

et al. 2014

Molecular Medicine Reports

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Vanishing lung syndrome, also known as idiopathic giant bullous emphysema, is a rare disease characterized by giant emphysematous bullae. The disease is diagnosed by radiological findings of giant bullae in one, or both, of the upper lobes of the lung, occupying at least one-third of the hemithorax. There have been several reports of vanishing lung syndrome, however it remains to be determined whether genetic inheritance is associated with the disease. In the present study, five patients within one family, with vanishing lung syndrome, were reported during a follow-up period of ~ 20 years. All of the patients were diagnosed by radiological findings, which showed diffuse bullae in the lungs, which were of varying size and asymmetrical distribution, and the occurrence of pneumothorax or emphysema. The Medical Ethics Committee of the People's Hospital of Zhangye Municipality (Zhangye, China) approved this study, and all subjects gave their informed consent During the follow-up period of 20 years, bullae in these patients were shown to progressively increase, and no other pulmonary diseases, including lung cancer, tuberculosis, pneumoconiosis and chronic bronchitis were observed. Autosomal dominant inheritance was observed in five cases, and autosomal recessive inheritance was observed in one case. The present study suggests that vanishing lung syndrome may be associated with autosomal dominant and recessive genetic inheritance.

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The Vanishing Lungs!

Cited by 2 publications

References 3 publications

Vanishing lung syndrome in a pregnant woman: case report and literature review

Vanishing lung syndrome in a pregnant woman: case report and literature review

Vanishing lung syndrome in one family: Five cases with a 20-year follow-up

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