Total Anomalous Pulmonary Venous Connection

Supracardiac Total Anomalous Pulmonary Venous Connection with Severe Rheumatic Mitral Valve Disease

“…TAPVC is a relatively rare anomaly accounting for only 2% of congenital heart disease 1 . Most cases present in infancy or early childhood with adult cases constituting only 0.3% of total cases 7 . Most cases presenting in adulthood have unobstructed supracardiac‐type pathology 8 .…”

“…Most cases presenting in adulthood have unobstructed supracardiac‐type pathology 8 . Although most patients with TAPVC have no associated major cardiac defects, many different associated anomalies have been reported including a patent ductus arteriosus and pulmonary stenosis 7 . It is rarely reported with congenital mitral valve anomalies, including mitral atresia, mitral stenosis, congenital mitral regurgitation, supramitral ring, and Williams syndrome, but it has never before been reported with severe rheumatic mitral valve disease.…”

Successful Correction of a Total Anomalous Venous Connection in a 63-year-old Male-Case Report and Review of the Literature

“…Most adult patients presented with the supracardiac type of TAPVC, and only seven authors describe adult patients with an intracardiac type of TAPVC as in our patient. 7,13,18,19,22,26,27 Rodriguez-Collado and coworkers reported a series of 19 adult patients aged 18 to 38 years with surgical correction of TAPVC between 1961 and 1989 including six cases of TAPVC to the coronary sinus. There were two deaths postoperatively in this early series of TAPVC repair.…”