Tufted angioma (angioblastoma)

Kaposiform hemangioendothelioma without Kasabach-Merritt phenomenon

“…It is well known that TA can occur in the absence of KMP. 7 However, we have also observed children with KHE who never develop thrombocytopenia. We hypothesized that small KHE would be less likely to be associated with thrombocytopenic coagulopathy.…”

“…Wilson Jones et al, 7,11 who were first to describe TA, later described 20 patients with TA without KMP, but they did not document lesional size. These tumors were most commonly located on the neck, upper aspect of chest, and shoulders.…”

“…5,7 Lymphatic channels seen in KHE and TA may be either part of the vascular tumor or represent an underlying lymphatic malformation. 4,5 Another possible explanation for the increased number of lymphatic channels is hyperplasia, secondary to lymphatic obstruction by the tumor.…”

“…The microscopic findings in TA are characteristic and consist of tightly packed capillaries located in the mid to reticular dermis in a cannonball pattern. 2,7 The spindled cells seen in KHE are occasionally observed in TA, and the crescentlike peripheral clefts seen in TA also have been noted in KHE. 4,5,8 Enjolras et al 9 noted that TA was more commonly the histologic pattern in early Kasabach-Merritt phenomenon (KMP) or residual lesions, whereas the appearance of KHE was more prominent during active disease.…”

Tufted angioma (Angioblastoma) of eyelid in adults-report of two cases

“…Wilson-Jones and Orkin [2] coined the term “tufted angioma” for this unusual pattern of angiomatous proliferation which was found to have some morphological similarities with strawberry nevi. However, as the name suggests, the lesion was seen as cannon ball like, small circumscribed angiomatous tufts and nodules in the dermis and subcutaneous tissue with characteristic lymphangioma-like vessels [3].…”