Unilateral absence of pulmonary artery and azygous continuation of interrupted inferior vena cava

Bista, Biraj; Ferris, Julie A.; Na, Nu; Krishnam, Mayil S.; Urgun, Deniz Akay

doi:10.1016/j.radcr.2020.02.021

Cited by 2 publications

(3 citation statements)

References 5 publications

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“…At present, only some UAPA cases diagnosed by echocardiography have been reported [9,10]. These reports comfirmed the diagnostic value of echoardiography in UAPA, and analyzed the complications caused by UAPA [11,12], and used for follow up assessment after surgery [13]. However, the clinical understanding of this disease is limited, and few references are focusing on the echocardiographic characteristics, changes of pulmonary artery pressure and prognosis.…”

Section: Introductionmentioning

confidence: 99%

“…Unilateral absence of pulmonary artery (UAPA) is also known as unilateral pulmonary artery proximal interruption or unilateral absence of intrapericardial segment of pulmonary artery, which is a rare congenital pulmonary vascular dysplasia [1]. The early clinical manifestations of UAPA are lack of specificity [2]. The symptoms are not typical, often with repeated pulmonary infection, hemoptysis, dyspnea, and easy to miss diagnosis and misdiagnosis [3].…”

Section: Introductionmentioning

confidence: 99%

“…the aims are: (1) to summarize the echoic feature, and to evaluate the usefulness and limitation of echocardiography in UAPA diagnosis. (2) to explore the dynamic change of pulmonary artery in UAPA patients.…”

Section: Introductionmentioning

confidence: 99%

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Unilateral absence of pulmonary artery analysis based on echocardiographic feature

Tian¹,

Zheng²

2021

Rev. Cardiovasc. Med.

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The unilateral absence of pulmonary artery (UAPA) is a rare congenital cardiovascular malformation, which is asymptomatic and easy to be ignored in early stage. A large number of complications may occur in the later stage. Therefore, early diagnosis and treatment is of great significance. The imaging data of 49 patients with UAPA discovered and confirmed clinically by the echocardiography in our hospital are analyzed. The results show that left pulmonary artery absence is more common (55%) and most of them are associated with other cardiovascular malformations (92%). Atrial septal defect and patent foramen ovale were most common in 56%. In which the absence of isolated pulmonary artery was 8% (4/49), and the absence of right pulmonary artery was 75% (3/4). Especially in the patients with tetralogy of Fallot, 77% (5/9) of them miss the diagnosis of UAPA. This suggests that doctors and sonographers should pay attention to the development of pulmonary artery bifurcation and left and right branches in multi-section, and strengthen the scanning of short axis section of high large artery.

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Section: Introductionmentioning

confidence: 99%

Section: Introductionmentioning

confidence: 99%

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Unilateral absence of pulmonary artery analysis based on echocardiographic feature

Tian¹,

Zheng²

2021

Rev. Cardiovasc. Med.

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Analysis of Ultrasonic Features Based on Absence of Pulmonary Artery

Tian

Minjuan

2021

j med imaging hlth inform

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According to clinical features and ultrasonic imaging features of patients with absence of pulmonary artery, it is necessary to analyze ultrasonic imaging features of absence of pulmonary artery to provide clinical basis for improving the diagnostic value and prognosis. The data and color Doppler echocardiography of 45 patients with absence of pulmonary artery are collected, who are confirmed by cardiac catheterization, CTA and operation, and the clinical features and ultrasonic imaging features are studied. The research results show that 57% of the patients have left absence of pulmonary artery and 91% of them have other cardiovascular malformations, where ASD/PFO is the most common, PDA and VSD are the second. Patients with UAPA have changes of pulmonary artery, the incidence of pulmonary artery abnormalities in multiple malformations, changes of ASD/PFO, PDA and VSD are mainly pulmonary hypertension. The ejection fraction of patients with UAPA is normal. The main manifestation of pulmonary hypertension is the increase of right cardiac volume load, and the main manifestation of pulmonary stenosis is the increase of collateral circulation. Pulmonary hypertension and its associated cardiovascular malformations may be related to the prognosis of patients. Ultrasound doctors should understand such diseases to improve the diagnosis rate and the prognosis.

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Unilateral absence of pulmonary artery and azygous continuation of interrupted inferior vena cava

Cited by 2 publications

References 5 publications

Unilateral absence of pulmonary artery analysis based on echocardiographic feature

Unilateral absence of pulmonary artery analysis based on echocardiographic feature

Analysis of Ultrasonic Features Based on Absence of Pulmonary Artery

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