Updated classification of papular mucinosis, lichen myxedematosus, and scleromyxedema

Self-healing juvenile cutaneous mucinosis

“…In a more recent review, the authors categorized the entity as a subtype of localized mucinosis, grouping juvenile and adult variants under the subset "self-healing papular mucinosis." 14 Four case reports are cited as examples of the adult variant. Unlike the distinct presentation of SHJCM, these patients had heterogenous clinical presentations that ranged from a single isolated hand lesion, to a patient with a distinct cutaneous eruption with arthralgias similar to SHJCM, to a patient with lichen myxedematosus with polyclonal gammopathy.…”

Escleromixedema: um caso tratado com prednisona oral

“…1,5 As a response to the indiscriminate use of the terms papular mucinosis, myxedematous lichen, and scleromyxedema, in 2001, Rongioletti et al, 6 based on anatomic-clinical criteria, adopted a new classification for this group of diseases: (1) generalized myxedematous lichen (scleromyxedema); (2) localized myxedematous lichen; (3) atypical forms of myxedematous lichen.…”

Rapid response of plasmacytomas to lenalidomide plus low‐dose dexamethasone therapy in a patient with relapsed multiple myeloma

“…Diagnosis requires the combination of the characteristic generalized papular sclerodermoid eruption, histological findings of increased fibroblasts and mucin, presence of a monoclonal gammopathy, and the absence of thyroid disease [16,17]. correspondence Scleromyxedema is associated with a myriad of systemic manifestations including dysphagia, dysarthria, dyspnea, weakness, peripheral neuropathy, carpal tunnel syndrome, arthritis, myalgias, myositis, myocardial infarction, restrictive lung disease, cerebral vascular accidents, memory loss, gait problems, fevers, encephalopathy, seizures, and coma [1,9,10,14,15].…”