Zosteriform connective tissue nevus: a case report

Abstract

Because of its distinctive clinical features and histopathological characteristics, zosteriform connective tissue nevus is considered a separate entity from other connective tissue nevi. Only two cases have previously been reported in the worldwide dermatological literature. Here we report a zosteriform connective tissue nevus in a 3-year-old boy with similar clinical presentation.

Connective tissue nevi: An entity revisited

“…The 3 cases (type C) with extensive monomelic infiltration were related to mixed forms (two cases) and the cellular form (one case). These differ from reported cases of zosteriform collagenoma [11][12][13] or papulolinear collagenoma [14][15][16][17] because of their progression to monomelic involvement of the entire limb, with profound infiltration and consequent functional impairment. It is important to point out that although histopathology was useful for the diagnosis of borderline clinical cases, it did not provide information on prognosis.…”

Zosteriform Connective Tissue Nevus: A Case Report

“…3 Since then, attempts have been made to classify the connective tissue nevi, 4-7 but they have mostly failed to explain all reported cases. The two most widely accepted methods of classification were 12 3…”

“…Although all previously reported cases have demonstrated some degree of elastic tissue abnormality, the diagnosis based on pattern of distribution of the lesions and absence of diagnostic criteria for other types of connective tissue nevi (Table 1). [10][11][12] This method of classification seems to be more pertinent to clinical experience. It makes the point clearly that the term zosteriform nevus refers to a clinical pattern of distribution of the lesion, rather than a separate hisotopathological type of connective tissue nevus.…”

Multiple Unilateral Zosteriform Connective Tissue Nevi on the Trunk

“…Zosteriform CTN, which displays a segmental distribution pattern, is rare, especially in the variety with a predominence of collagen5. It was first reported in 1944 by Steiner3, who described the case of a 5-year-old girl with unilateral distribution located on the right side of the lower chest and back.…”