Freeman-Sheldon syndrome (FSS), as first described by Freeman and Sheldon in 1938, is a morphologically well-defined syndrome that results in a dysmorphic status combining bone anomalies and joint contractures with characteristic facies. It is part of the nosologic group of pathologies currently known as distal arthrogryposis as reported by Hall et al. (Am J Med Genet 11:185-239, 1982 [1]). It is a rare disorder and its exact prevalence is unknown. Our objective is to report a case of FSS presenting with microstomia and add a brief review of the literature for similar cases.

Epidermolysis bullosa (EB) constitutes a group of phenotypically diverse genodermatoses, which manifests with blistering and erosions of the skin and mucous membranes as the unifying diagnostic feature. It is an acquired disease or inherited as either autosomal-dominant or recessive with an incidence of 1/50 000. The prominent clinical characteristic of the disease is the development of bullae or vesicles in mucosa or skin in response to minor trauma. It is a chronic mechanobullous disease characterised by auto antibodies against Type VII collagen. This paper documents a case of a man diagnosed with dominant dystrophic EB; describing the measures that dentists and healthcare providers should adopt in order to provide a safe and effective dental treatment. Early prevention protocols for these patients have also been discussed.

Odontogenic keratocysts (OKCs) are developmental odontogenic cyst of epithelial origin. Multiple OKCs are often associated with a syndrome, especially nevoid basal cell carcinoma syndrome. The present article presents a series of two nonsyndromic cases of multiple OKCs. The presence of multiple OKCs and their recurrence can be attributed to factors such as the friable cystic lining, and daughter cysts. However, a comprehensive evaluation of any patients reporting multiple cysts/OKCs always has to be undertaken and the syndromic association should be ruled out.

Ranulas are mucus-contained swellings, known as Mucoceles, which usually occur on the oor of the mouth. The term Ranula is a Latin derived from the word “Rana” which means frog and since these swellings resemble the belly of a frog, they are known as Ranulas. This article presents a case of simple ranula in a 30-year-old Male patient treated with Marsupialization.