Comorbid pulmonary complications in people with sickle cell disease (pwSCD) are associated with high rates of morbidity and mortality, and poor access to care contributes to poor outcomes among this particularly high-risk pwSCD. Our purpose was to describe the population served and the resources required for hematology, pulmonary, nursing, respiratory therapy, social work, genetics, psychology, and school liaison providers to see these patients in an integrated clinic. We abstracted demographic, medication, clinical, and diagnostics data of the pwSCD seen at least once in this clinic from February 1, 2014 to December 10, 2020 from the electronic medical record and identified 145 unique pwSCD. Abnormal lung function and bronchodilator responsiveness were detected in 31% and 42% of participants respectively. Sleep abnormalities were found in over two-thirds of those screened and 65% had ≥1 previous acute chest syndrome episode. This clinic also allowed for direct provider communication and required relatively limited resources to serve a large number of severely affected pwSCD. Given the degree of abnormal respiratory variables detected and the limited resources required to implement this model, studies are warranted to evaluate whether it has the potential to improve outcomes in high-risk populations.

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People with sickle cell disease (pwSCD) are at risk of developing lung conditions that complicate their sickle cell disease (SCD) but often face healthcare access barriers. An interdisciplinary SCD-pulmonary clinic was created in 2014 at Nationwide Children's Hospital (NCH) to address access barriers that may prevent optimized treatment. We hypothesize that pwSCD and pulmonary disease would have fewer hospitalizations for acute chest syndrome (ACS), asthma, and vaso-occlusive episodes (VOEs) in the two years after their initial SCD-pulmonary clinic visit compared to the two years prior. From 2014-2020,119 pwSCD were evaluated in the SCD-pulmonary clinic and followed at NCH for at least two years before and after this visit. Acute care outcomes, pulmonary function, polysomnography, echocardiogram, laboratory, and medication prescribing data were collected and analyzed using the Wilcoxon signed ranked and McNemar's tests. The median number of acute care visits for ACS (p<0.001) and asthma (p=0.006) were significantly lower during the two years after pwSCD's initial SCD-pulmonary clinic evaluation compared to the two years prior. Asthma and allergic rhinitis were more frequently diagnosed and prescriptions for hydroxyurea (p=0.005) and inhaled corticosteroids (p=0.005) were more common in the post SCD-pulmonary clinic period. The median number of prescribed systemic corticosteroids was lower in the two years following SCD-pulmonary clinic evaluation (p<0.0001). Lactate dehydrogenase and white blood cell counts also significantly decreased. Implementing a multidisciplinary SCD-pulmonary clinic is feasible and may allow improved management of pulmonary problems and lead to improvements in health and acute care utilization.

MINISEMINARS decided to organize a miniseminar to provide guidelines to surgeons experiencing this complication and for surgeons wishing to be informed to device failures. The symposium will be divided into two major parts. In the first part, clinical cases associated with medical device failures will be presented. The impact of one of these cases based on a national survey of pediatric otolaryngologists will be highlighted. The second part will then include the medicolegal ramifications, disclosure to patients and families, and resources available for the surgeon to report and receive updates on device failures. Educational Objectives: 1) Learn the role of the surgeon in disclosing device complications to patients and national reporting agencies. 2) Learn the medicolegal ramifications of a device failure to the surgeon. 3) Learn how an otolaryngologist can keep him or herself informed of device recalls or complications.

Program Description: Recently, there has been growing interest in developing and using simulation technologies for basic surgical skills training for residents. In addition, as our specialty continually evolves and we make efforts for quality and lifelong learning, simulation technologies may also be useful for keeping experienced surgeons up-to-date with their skills. We will present currently available surgical simulators for temporal bone dissection, endoscopic sinus surgery, airway endoscopy, and tonsillectomy. The presenters will provide descriptions and show videos demonstrating the function of these devices. In addition, each panelist will present data evaluating the efficacy of these simulators as being effective teaching instruments.Educational Objectives: 1) Differentiate the variety of simulation technology devices available for surgical skills training in otolaryngology-head neck surgery. 2) Recognize the advantages and limitations of using simulation technologies for acquiring and maintaining surgical skills. 3) Assess the validity of the studies presented to evaluate the efficacy of simulation devices as valuable learning tools. Professionals and Women Otolaryngologists, will introduce eminent speakers to describe the state of otolaryngology in these regions and subject areas, including socioeconomic and workforce issues.Educational Objectives: 1) Recognize the myriad ways the Academy interacts with otolaryngology communities in different regions. 2) Consider the opportunities for collaboration in scientific exchange, research, fellowships, and observerships. 3) Articulate the Academy's resources available to members, subscribers, meeting attendees, and web visitors.