Hidradenoma papilliferum is a rare, benign adnexal tumor considered to be of apocrine origin that occurs almost exclusively in females on the anogenital area. Ectopic or non-anogenital hidradenoma papilliferum is rare. But ectopic hidradenoma papilliferum associated with pilomatricoma has not been described in literature to our knowledge. We describe a case of hidradenoma papilliferum associated with pilomatricoma presenting with an intradermal nodule, 1cm in diameter on the right side of the back of the neck with history of 15 years duration. This case is reported because of its rarity.