Osteocartilaginous exostoses are benign bone tumors frequently found in the metaphysis of long bones but rarely in the spine. Four patients with acute spinal cord decompensation due to vertebral exostoses spinal cord compression have been previously described in the literature. We report an additional case of rapidly evolving spinal cord compression due to a cervical osteochondroma in a patient with hereditary multiple exostoses (HME), also known as Bessel Hagen disease. Careful analysis of the 5 cases suggested to us that patients with HME should have a systematic spinal imaging screening, in order to prevent rapid neurological decompensation. A minimal risk surgical procedure can be performed at a time of election.
We read with interest the recent article entitled "MR Imaging of the Optic Nerve Sheath in Patients with Craniospinal Hypotension" by Rohr et al. 1 In patients with craniospinal hypotension, apart from engorged venous sinuses, enlarged pituitary gland, subdural effusions, and sagging of the brain, the authors have observed a partially or fully collapsed intersheath space of the optic nerves. Such a demonstration is particularly clear in their Fig 3. We would like to draw more attention to changes in the pituitary gland. As shown in Fig 3C (arrow), enlargement of the sellar content is also due partially to dilation of the inferior intercavernous sinus (IICS), which has collapsed after treatment. Such a dilation is not mentioned in the legend. In our experience, the IICS, which is visible in roughly 30% of children on MR imaging, is never quite visible in the healthy adult.In a personal series of 12 adult patients with intracranial hypotension syndrome studied by MR imaging, the IICS was visualized in 11 cases 2 : The IICS was very thin in 2 cases, prominent in 6 cases, and very thick (Ͼ3 mm) in 3 cases (Fig 1). The differential diagnosis includes a pituitary gland with increased height on one hand, corresponding to physiologic (hyperplasia, pregnancy, small sella) or pathologic conditions (a holosellar pituitary adenoma, hypophysitis, and so forth), and focal intrasellar lesions such as pituitary microadenoma on the other hand. Recognition of the presence of the IICS allows exclusion of these pituitary abnormalities. In 3 of 12 cases of our series, MR imaging follow-up after blood patch or spontaneous resolution of intracranial hypotension demonstrated a significant decrease in the height of the IICS (Fig 2). In our experience, dilation of the IICS constitutes a useful adjunctive sign for the diagnosis of intracranial hypotension. Moreover, enlargement of the IICS should be added to the other causes of enlargement of the sellar content.
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