SummaryThe Klippel-Trenaunay syndrome is a rare congenital disorder that affects one or more limbs. It is characterised by cutaneous vascular nevi, venous malformations and hypertrophy of soft tissues and bone. There are very few cases reported in pregnant women, so the level of uncertainty is high when it appears during gestation. It is a disease that increases obstetric risk and can exacerbate complications, mainly thromboembolic and haemorrhagic. We report below the case of a pregnant woman diagnosed with this syndrome and the multidisciplinary management held in our centre.
BACKGROUND
The optic chiasm (OC) is an X-shaped structure formed by the crossing of the optic nerves in an axial view of the fetal brain. It is located in the chiasmatic cistern and it is surrounded by the Willis circle. The anterior cerebral arteries lay anteriorly, the posterior communicant arteries lay laterally and the posterior cerebral arteries are identified posteriorly. The decussation or centre of the OC corresponds to the origin of the middle cerebral arteries laterally arising from internal carotids. This article is protected by copyright. All rights reserved.
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