No abstract

ResumenEl tumor de células del estroma gonadal es un tipo de neoplasia poco común, menos del 2.3% de todos los tumores ováricos, y la variante de túbulos anulares es aún más infrecuente, apenas un 0.05-0.6%. Aquí presentamos un caso, tratado quirúrgicamente hasta ser irresecable. El estudio histopatológico muestra tumor de cordones sexuales con patrón de túbulos anulares, con calretinina e inhibina positivos. Evolución clínica desfavorable, con muy pobre respuesta a la quimioterapia. Por ello es prioritario identificar histologías poco habituales de forma temprana, para brindar y ensayar mejores opciones terapéuticas.Palabras clave: Tumor de cordones sexuales con túbulos anulares. Neoplasia de ovario. Recurrente. Ovarian sex cord tumor recurrent: A case report and review of the literature abstractOvarian gonadal stromal cell tumors are uncommon neoplasms. Sex cord stromal tumors represents less than 2.3% of all ovarian tumors and sex cord tumors with annular tubules are an extremely uncommon neoplasm, with less than 0.05-0.6%. We present a case, with late recurrence, in a woman who clinically started when she was 33 years old, with acute abdominal pain; then a left oophorectomy without malignancy was performed. Five years later, she newly presented abdominal pain and a laparoscopy was performed without apparently tumoral activity, two years later the pain was exacerbated; there was pelvic-abdominal dissemination, unresectable. Histopathologic study report demonstrated sex cord tumor with annular tubules, and positivity for calretinin and inhibine. The clinical evolution was bad, with poor response to chemotherapy. With this case we learned that we must identify early the different uncommon histologies, with tracking, to have the possibility to offer better treatments.