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We thank Richard Medeiros, Medical Editing International, for editing various versions of the manuscript. We thank the patient depicted in the Figure for granting permission to publish this information. These individuals were not compensated for their contributions.

Cutaneous squamous cell carcinoma with epidermodysplasia verruciformis-like features in a patient with Schimke immune-osseous dysplasia K E Y W O R D S : acquired epidermodysplasia verruciformis, Schimke immune-osseous dysplasia, squamous cell carcinoma Schimke immune-osseous dysplasia 1 (SIOD) is an autosomal recessive disorder caused by mutations in the SMARCAL1 gene encoding an ATP-driven annealing helicase that stabilizes stalled replication forks and facilitates DNA repair during replication. 2 The syndrome is characterized by spondyloepiphyseal dysplasia, steroid-resistant nephropathy and cellular immune deficiency. Additional features include cerebral ischemic events, microdontia, short stature, hyperpigmented macules on the trunk and extremities and characteristic dysmorphic features such as a broad, depressed nasal bridge and a broad nasal tip. Renal pathology shows focal segmental glomerulosclerosis; BRIEF COMMUNICATIONS 465 ORCID Mary-Katharine Collins

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