Le syndrome de Sturge-Weber (SWS) ou angiomatose encéphalo-faciale, est un syndrome neuro-cutané et oculaire congénital rare. Il comporte deux types de malformations: capillaire faciale congénitale à type d’angiome plan et capillaro-veineux lepto-méningé de localisation le plus souvent pariéto-occipitale homolatérale. La Neuroimagerie, essentiellement l’imagerie par résonnance magnétique (IRM), joue un rôle important dans l'établissement du diagnostic, idéalement avant l'apparition de complications neuro-oculaires. Nous rapportons le cas d’un enfant chez qui le SWS est suspecté devant la présence d’un angiome facial et d’une épilepsie pharmaco-résistante.

Lipomatous pseudohypertrophy (LPH) of the pancreas is an uncommon affection of exocrine pancreatic insufficiency. It is defined as substitution of the pancreatic exocrine gland by a large fat component. We report the case of a young patient with malabsorption syndrome (chronic diarrhoea and steatorrhoea), abnormal laboratory results and normal fibroscopy. Computed tomography revealed characteristic diffuse pancreatic abnormalities.

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Eccrine porocarcinoma is a rare type of skin neoplasm. It represents less than 0.01% of all epithelial cutaneous tumours. Early diagnosis is the only way to minimize the mortality rate, given its aggressive nature and the high rate of local recurrence and metastasis. Clinical diagnosis is challenging and the confirmation is histological. Few studies have been published about the radiological features of eccrine porocarcinoma. We report a case of a localized eccrine porocarcinoma along with ultrasound, MRI features, and a review of the literature to highlight the role of imaging in the diagnosis and treatment plan.

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