A 35-year-old patient, a native of Uzbekistan, had shortness of breath and swelling of the lower extremities at the 35th week of the fourth pregnancy. She gave birth at the 39th gestational week naturally. Symptoms progressed within 3 months after delivery: ascites and hydrothorax appeared. According to echocardiography, dilation of the heart chambers was detected, the left ventricular ejection fraction was 30%. A diagnosis of peripartal cardiomyopathy (CMP) complicated by CHF third degree was established. During 10 days of treatment, the manifestations of HF decreased significantly.

The article presents a clinical case of congenital arteriovenous dysplasia – Parkes Weber syndrome of the lower extremities. The features of its clinical picture and the difficulties of diagnosis are described. It is emphasized that Parkes Weber syndrome is a rare congenital disease of the vascular system, in some cases with the absence of its typical clinical manifestations and combined with other pathologies of the veins.