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Capillary malformation‐arteriovenous malformation (CM‐AVM) is a rare condition characterized by multiple cutaneous capillary malformations with potential associated arteriovenous malformations. RAS p21 protein activator 1 (RASA1) and ephrin type‐B receptor 4 (EPHB4) genes are implicated. We present a child with CM‐AVM, due to EPHB4 mutation, and Ebstein's anomaly. Although EPHB4 is a known effector of vascular remodeling, its contribution to cardiogenesis is still being explored. Further research is needed to determine causality of Ebstein's anomaly in the setting of CM‐AVM due to EPHB4 mutation.