Malignant rhabdoid tumour is a rare, but highly aggressive, malignancy of early childhood. Malignant rhabdoid tumour can be classified according to renal and extrarenal locations. For extrarenal lesions, the spinal cord and central nervous system are most commonly involved, although such tumours may arise in almost any site. However, malignant rhabdoid tumour of the bladder has only been reported in a few patients, mainly focusing on its pathological aspects. We report on a patient with malignant rhabdoid tumour of the urinary bladder. The clinical, radiological, and histological features of this disease entity are discussed.