Ectrodactyly-ectodermic dysplasia-cleft lip/palate (EEC) syndrome is a rare congenital anomaly of inherited origin and varying clinical features. This syndrome has three main symptoms, which display variable expression and penetrance. The management of this syndrome is challenging, with few reports in the medical literature. We present a case of a 22-year-old boy with EEC syndrome and offer insight into current knowledge about this syndrome.

Purpose: This study is aimed to determine the efficacy of temporalis muscle and fascia flap in the treatment of unilateral temporomandibular joint (TMJ) ankylosis in adults. Treatment of TMJ ankylosis has been a topic of debate and the treatment options are multidimensional. Achieving good postoperative mouth opening and functional and cosmetic outcomes of surgery, depends on the method of reconstruction. The need of study is to give the best possible solutions with minimal morbidity to the underlying deformity. Materials and methods:A retrospective study was done on 51 patients to evaluate the postoperative results for unilateral TMJ ankylosis. Parameters such as etiology, postoperative mouth opening on 1st, 2nd, 6th week and 6 months and intraoperative and postoperative complications were recorded. The operative protocol for unilateral TMJ ankylosis entailed: (1) Resection of the ankylotic mass, (2) intraoral ipsilateral coronoidectomy, (3) contralateral coronoidectomy when necessary, (4) interpositional tissue transfer to the TMJ with temporalis muscle and fascia flap, (5) maxillomandibular fixation (MMF) and (6) early mobilization and aggressive physiotherapy. Results:The results were encouraging and functional results of interpositional arthroplasty were satisfying with minimal complications. Early postoperative initial aggressive exercise, physiotherapy, and strict follow-up play an important role in preventing postoperative adhesions. Conclusion:The findings of this study support the use of temporalis muscle and fascia flap in adult patients with unilateral TMJ ankylosis.

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Introduction: Aneurysmal bone cyst is a rare, non-neoplastic lesion affecting the metaphysis of long bones and vertebrae, characterized by blood-filled spaces separated by fibrous septae. Aims and objectives: In this study, we present a case of an aneurysmal bone cyst in a 7-year-old child with characteristic X-ray findings to increase awareness as early diagnosis and treatment can limit disability. An aneurysmal bone cyst is a rare, benign neoplastic lesion affecting the metaphysis of long bones and vertebrae, characterized by blood-filled spaces separated by fibrous septae.[1] Diagnosis depends on typical features of magnetic resonance imaging, and confirmation by biopsy is essential before surgery is considered.   We present an aneurysmal bone cyst in a 7-year-old child with characteristic X-ray findings. Diagnosis of ABC should be suspected in young patients presenting with limb pain or swelling, and pain disproportionate to the mechanism of injury could indicate pathologic fracture. Early detection of ABC is possible as an incidental finding by closely examining routine X-rays so that appropriate treatment can be instituted early and complications like pathologic fractures can be avoided. This case will help to increase awareness as early diagnosis and treatment can limit disability.