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Introduction. Despite the continuous improvement of methods for prenatal diagnosis of fetal malformations, at present, the limitations of intrauterine verifcation of vascular lung anomalies and relevance in postnatal typing of all components of pathological pulmonary hemodynamic, especially in the case of complex, combined vascular malformations, remain. Detailed and expert assessment of the anatomy of the pulmonary vessels, intrapulmonary hemodynamic is necessary to minimize the time for the surgical correction of the defect in order to avoid the development of irreversible pulmonary hypertension. One of the most rare and diffcult to diagnose forms of a combination of vascular abnormalities is congenital pulmonary venolobar syndrome (CPVS), which combines venous, arterial, pulmonary and cardiac pathology, to one degree or another coexisting in one patient.Objective – analysis of clinical material and data of different diagnostic methods in children with CPVS. This everything will help to optimize diagnostics and choose the most safe and informative method to visualize combination of pulmonary and cardiovascular diseases and to determine the specifcity of pulmonary circulation. Furthermore, it will allow to minimize all risks and negative consequences for patient’s body.Material and methods. We reviewed the records of 11 children (age from 14 days to 17 years old) with intraoperative verifcation of CPVS. We systematized all variants of vascular anomalies of lungs in children with CPVS, its possible combinationswith other abnormalities. We performed the comparison of capability and diagnostic signifcance of plain radiography, echocardiography, selective angiography and CT­scan in determining the specifcity of pulmonary circulation in children with CPVS and assessment of combination of the malformation components. Results. Antenatal echocardiography and postnatal diagnostics using echocardiography, plain radiography and selective angiography is extremely limited. We suggested the diagnostic algorithm using CT­scan with the proof of the great representativeness. Obligatory components of CPVS were identifed: reduction of the right lung volume, anomalous pulmonary venous drainage (scimitar syndrome) and non­obligate components of malformation: aplasia or hypoplasia of the right pulmonary artery, systemic pulmonary arterial supply with differential pulmonary perfusion, pulmonary sequestration, other congenital heart abnormalities.Conclusion. CPVS is a rare congenital malformation. Antenatal diagnosis of all components of CVLS is impossible. MDCTAG is the most effective diagnostic method that allows to identify all components of CPVS in postnatal period. This method does not require additional radiodiagnostics and invasive diagnostic procedures.

Relevance. Pulmonary sequestrations are rare pathology and make from 0.15 to 6.4 % of all congenital abnormality. Thus intra-abdominal localization of this malformation is described only in 2.5 % of all pulmonary sequestrations. Objective. Reflect the difficulty of differential diagnosis of rare lung malformation in newborns. Materials and methods. 2 cases of the extralobar sequestration located under the diaphragm diagnosed for newborns in a children's hospital for the last 20 years are in details described. Results. The diagnosis of an intra-abdominal extralobular pulmonary sequestration was finalized only after surgical treatment, confirmed histologically. Questions of differential diagnostics of rare congenital pulmonary malformations are discussed with tumors of suprarenal localization at newborns, comparison of own results to data of literature. Conclusions. In the differential diagnosis of suprarenal lesions at newborns it is necessary to consider the possibility of intra-abdominal extralobar pulmonary sequestration, especially in the localization of pathological changes at the left side.

Среди провоцированных психогенным стрессом пси-хических нарушений диссоциативные расстройства зани-мают одно из ведущих мест.На современном уровне знаний анализ этих рас-стройств в исследованиях, ориентированных на первич-ность стрессорного воздействия, проводится на базе мо-дели перитравматической диссоциации [1][2][3] Цель исследования. Связанные со стрессом диссоциативные расстройства (ДР) отличаются высокой распространенностью в психиатрии и общей медицине, однако психопатологическая дифференциация ДР и вклад расстройств личности в их формирование остаются малоизученными. Цель исследования -клинический анализ провоцированных стрессом стойких диссоциативных расстройств, а также конституциональных аномалий, составляющих «почву» для их формирования. Материал и методы. Обследовали 20 пациентов с обусловленными стрессом онкологического заболевания (нозогенные) диссоциативными расстройствами, по 10 в группах детачмент-диссоциации (ДД) (отрицание болезни и/или связанной с ней угрозы жизни, некомплаентность) и компартмент-диссоциации (полное/частичное отчуждение компонентов реакции на стресс -эмоциональные, когнитивные, адекватная комплаентность). Группы сопоставимы по демографическим и онкологическим показателям. Использовали клинический и психологический методы. Результаты и заключение. Диссоциативные расстройства представляют собой вторичные психопатологические феномены. ДД формируется в рамках шизофренических нозогенных реакций на основе сверхценных идей соматического благополучия (либо полная излечимость злокачественного новообразования) и обнаруживает сродство с шизотипическим расстройством личности. Компартмент-диссоциация манифестирует в пределах невротических нозогенных реакций на базе психогенных комплексов бинарной структуры -патология воображения (синдром «прекрасного равнодушия») в сочетании с тревогой о реально существующем заболевании и обнаруживает сродство с расстройствами личности истерического круга. Ключевые слова: диссоциативные расстройства, расстройство личности, стресс, нозогения, онкология.Objective. Stress-induced dissociative disorders (DD) have high prevalence in psychiatry and general medicine but the psychopathological differentiation of DD and contribution of personality disorders in their development is less studied. Authors conducted a clinical analysis of stress-induced persistent DD and underlying constitutional abnormalities. Material and methods. It was examined 20 patients with DD induced by the stress caused by a cancer diagnosis, including 10 patients of detachmentdissociation group (denial of the disease, non-compliance) and 10 patients with compartment-dissociation (complete or partial detachment of stress response components (emotional, cognitive), adequate compliancy). The groups were matched for demographic and cancer characteristics. Clinical and psychological methods were used. Results and conclusion. DD are secondary psychopathological phenomena. Detachment-dissociation develops in the frames of schizophrenic nosogenic reactions based on overvalued ideas of somatic we...