Choledochal cyst in infancy and childhood. Analysis of 16 cases.

Abstract

Onset of symptoms occurred from 7 days of age to 9 5 years; in 10 patients onset occurred under 12 months of age, in 3 from 13 to 24 months, and in the remaining 3 from 2 to 9*5 years. The first symptoms were jaundice, vomiting, acholic stools, and poor sucking. Obstructive jaundice and acholic stools were found in more than 80 % of the patients, and abdominal mass in 60 %. Vomiting occurred in 50% of the patients, one-third of whom showed failure to thrive, and 70% of patients over the age of 1 -5 years had abdominal pain. About half of the patients had a mild to moderate degree of fever.In all patients primary excision of the cyst was followed by hepaticojejunostomy in Roux-en-Y fashion. The postoperative course was uneventful in 14 patients; 2 patients died, one from ascending cholangitis and one from hepatic failure.

Appendix Carcinoid Found Incidentally During Excision of a Choledochal Cyst: Report of a Case

“…In addition, percutaneous or endoscopic cholangiography may be used in the diagnosis. [3][4][5][6] Rouxen-Y hepaticojejunostomy is the treatment of choice for choledochal cysts. 7 Carcinoid tumors are thought to arise from embryonal neural crest cells, or so-called argentaffin cells, which migrate to sites within the respiratory and gastrointestinal tracts during neonatal development.…”

Differential Diagnosis of Neonatal Jaundice

“…Первое описание кист билиарного тракта (кист холедохуса) было дано Vater A. в 1720 г. Частота кист холедохуса составляет 1/13 000 новорожденных, в 7% удается диагностировать кисты холедохуса в антенатальном периоде. Первые клинические признаки кист холедохуса -ахоличный стул, рвота, желтуха и пониженное питание [16]. Желтуху и ахоличный стул имеют более 80% новорожденных.…”

Biliary Disease in Infants and Children

“…Choledochal cysts have been described in a series of anecdotal cases [33,34] and have been classified according to their gross morphology [35][36][37][38][39][40]. As their name suggests, they are cystic malformations of differing phenotypes that affect some or most of the bile duct.…”