Clinical experience in diagnosis and management of superior semicircular canal dehiscence in children

Abstract

In contrast to adults, children with SSCD usually present with auditory symptoms first, although they share some similarities with adults in clinical manifestations of SSCD. Our study shows that SSCD syndrome, a well-accepted clinical entity, exists in the pediatric population. Conservative management is preferred for children with SSCD; nevertheless, surgical intervention is necessary for those with disabling vestibular symptoms. To date, this is the first clinical case series of symptomatic pediatric patients with SSCD.

Síndrome da deiscência do canal semicircular superior: relato de dois casos

“…Auditory complaints were not reported by the patients of the present study as being the first symptoms, however in the literature there are studies in which the patients reported that the first symptoms were the auditory alterations 14 …”

“…Such findings are important for the audiological and otoneurological practice, indicating the need to investigate the presence of SSCDS in patients with these symptoms 4,10,11,14 .…”

Superior canal dehiscence syndrome in children – A case report

“…[13] All of those children with CT-morphological dehiscence did not show any audiological or vestibular symptoms. So far, to our knowledge, there are only two case reports and a case series with a total of seven children with SCD [14][15][16]. The experience with the diagnosis and therapy of dehiscence syndrome in children is limited and still requires standardization.…”

“…In the case series presented by Lee, hearing problems were the reason for referral to an ENT specialist [14]. In the above-presented case report, episodes of dizziness were the main complaint made.…”

“…However, if the suspicion of childhood dehiscence is further substantiated in the medical history, clinical examination, and diagnostic testing, imaging is recommended. Thus, a CT scan of the temporal bone was also conducted in the case series described by Lee [14]. Imaging also helps in diagnosing other malformations such as semicircular canal atresia as well as excluding or confirming a child's semicircular canal dehiscence [38][39][40].…”