Management of recurrent acute bilateral corneal endotheliitis monitored by serial corneal pachymetry

Keratoendotheliitis Fugax Hereditaria: A Novel Cryopyrin-Associated Periodic Syndrome Caused by a Mutation in the Nucleotide-Binding Domain, Leucine-Rich Repeat Family, Pyrin Domain-Containing 3 ( NLRP3 ) Gene

“…1,2 Two decades later, a second Finnish family with 21 affected members in 5 generations was reported, now highlighting transient corneal endothelial changes, and the term keratoendotheliitis fugax hereditaria was proposed. 3 Keratoendotheliitis in general is recognized in association with different types of viral keratitis 4 and it also can occur as an idiopathic sporadic finding, [5][6][7] but we are unaware of any other reports of familial keratoendotheliitis.…”