Medical Care for Athletes with Hemophilia

Fiala, Kelly A.; Ritenour, Donna

doi:10.1123/att.9.2.16

Cited by 4 publications

(4 citation statements)

References 8 publications

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“…Quanto à atividade física, 69,6% responderam não estar participando de nenhuma no momento, o que remete ao fato de que, no passado, pelos riscos temidos, os hemofílicos eram desestimulados à prática de atividade física. 11 Com a introdução do fator liofilizado de uso domiciliar para tratamento profilático, tornou-se possível que hemofílicos pudessem ter uma vida com participação ativa em casa, escola, trabalho, esportes e lazer, 12 sendo a atividade física considerada como benéfica a eles. 13 Em estudo realizado nos Países Baixos demonstrou-se que não houve diferença na participação em atividades físicas entre hemofílicos, que faziam a profilaxia com o fator liofilizado e controles saudáveis.…”

Section: Discussionunclassified

Qualidade de vida de pacientes hemofílicos acompanhados em ambulatório de hematologia

Nunes¹,

Rodrigues²,

Soares³

et al. 2009

Rev. Bras. Hematol. Hemoter.

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IntroduçãoHemofilia é uma coagulopatia hereditária recessiva ligada ao sexo, ocorrendo devida à falta ou produção defeituosa de moléculas dos fatores VIII ou IX da coagulação. A deficiência de fator VIII (Hemofilia A) é a mais frequente, ficando com 85% dos casos; já a deficiência do fator IX (Hemofilia B) corresponde a 15% . 1,2A incidência na população mundial é de 1/10.000 (pelo fator VIII) e de 1/30.000 (pelo fator IX) nascimentos do sexo masculino. É caracterizada pela ocorrência de hemorragias que aparecem espontaneamente ou em consequência de traumatismos leves e são comuns nas articulações. As hemorragias geralmente ocorrem nas grandes articulações, podendo causar muita dor, danos permanentes e incapacitantes se não forem tratados adequadamente. [1][2][3] Segundo Ritterman, 4 três componentes podem afetar os hemofílicos: o primeiro corresponde à atitude do indivíduo frente a sua enfermidade, seu sentimento de impotência frente aos sangramentos e a visão de não ser uma pessoa normal. O segundo refere-se ao contexto familiar em que, dentre as considerações, há a de que a hemofilia interfere na relação entre os pais e irmãos; o complexo de culpa que

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Section: Discussionunclassified

Qualidade de vida de pacientes hemofílicos acompanhados em ambulatório de hematologia

Nunes¹,

Rodrigues²,

Soares³

et al. 2009

Rev. Bras. Hematol. Hemoter.

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“…Although formerly limited to swimming and golfing, most sports (e.g. bowling, tennis, hiking, fishing) are considered possible for patients with haemophilia, if proper training and equipment are used, and with appropriate medical management [5,6]. In addition to prophylactic treatment, participating in physical activity is also considered as a preventive measure against chronic joint damage associated with haemophilia.…”

Section: Introductionmentioning

confidence: 99%

Physical activity and joint function in adults with severe haemophilia on long-term prophylaxis

Khawaji

Astermark

Åkesson

et al. 2011

Blood Coagulation &Amp; Fibrinolysis

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It has been shown that patients with severe haemophilia treated on demand are not as physically active as their healthy peers and often have a sedentary lifestyle that contributes to chronic joint disease. The use of prophylaxis provides opportunities for participation in physical activities with fewer bleeding episodes. The objective of the study was to describe the type, intensity and duration of physical activity among adult patients with severe haemophilia and to find out whether a joint function dependency exists. Patients with severe haemophilia, divided into two groups (group A: patients who started prophylaxis at the age of ≤3 years and group B: patients who started prophylaxis at the age of >3 years), and 190 controls were included. Physical activity was assessed using the self-report Modifiable Activity Questionnaire. Time involved and intensity of all aspects of physical activity for group A were almost similar to their healthy peers. Group B had significantly lower vigorous, leisure and total physical activities than group A and their healthy peers. Positive significant correlations were found between leisure and total physical activities and joint score in group A, whereas in group B, there was negative significant correlation between only nonweight-bearing activity and joint score. The early start of long-term, primary prophylaxis has been successful in reducing frequency of bleeds and thereby preventing or delaying subsequent chronic joint disease, and enables the patients to lead a physically normal life also during adulthood when patients with haemophilia treated on demand are expected to have substantial joint disease impacting their physical activity.

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“…Before the era of prophylaxis regimes, the life of a patient with haemophilia was to a great extent dependent on the severity of the disease and the frequency of bleeding episodes, often resulting into an inactive lifestyle [1,2]. The introduction of factor replacement, home treatment and prophylaxis regimes made it possible for persons with haemophilia to live a life in which participation in household, school or work; even sports and leisure activities became feasible.…”

Section: Introductionmentioning

confidence: 99%

“…Relationship between the child or parent reports of Haemo-QoL and both absolute and relative VO 2peak ranged from R ¼ 0.00 and R ¼ 0.4.Exercise testing in children with severe haemophilia A was a safe procedure. Patients with Introduction Before the era of prophylaxis regimes, the life of a patient with haemophilia was to a great extent dependent on the severity of the disease and the frequency of bleeding episodes, often resulting into an inactive lifestyle [1,2]. The introduction of factor replacement, home treatment and prophylaxis regimes made it possible for persons with haemophilia to live a life in which participation in household, school or work; even sports and leisure activities became feasible.…”

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confidence: 99%

Physical fitness, functional ability and quality of life in children with severe haemophilia: a pilot study

et al. 2006

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In the Netherlands comparable levels of sports-participation between persons with haemophilia and healthy controls have been reported. This raises the question if children with haemophilia under the currently available prophylaxis do reach comparable levels of physical fitness and health-related quality of life (HRQoL) as their healthy peers. The aim of this study was to investigate the level of physical fitness, functional ability and quality of life and to determine the feasibility to safely test the exercise capacity of boys with severe haemophilia A. Thirteen subjects participated in this study. Physical fitness was determined using the measurement of maximal oxygen uptake (VO2peak) attained during a graded maximal exercise test to volitional exhaustion. Joint health, physical activity levels and health-related quality of life (Haemo-Qol) were also measured. Mean VO2peak was 1.86+/-0.77 L min-1 (Z-score: -0.39+/-1.61) which was not significantly different from reference values. Relative VO2peak was 47.42+/-8.29 mL min-1 kg-1 (Z-score: -0.52+/-1.43), which did not differ significantly from reference values either. One boy suffered a joint bleeding one day after the test. Haemo-Qol scores in parents and children ranged from 3.2% to 36.7% (100% reflects poor outcome). Relationship between the child or parent reports of Haemo-QoL and both absolute and relative VO2peak ranged from R=0.00 and R=0.4. Exercise testing in children with severe haemophilia A was a safe procedure. Patients with severe haemophilia A with good joint health and no limitations of activities have comparable physical fitness and physical active lifestyle with healthy peers and good HRQoL.

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Medical Care for Athletes with Hemophilia

Abstract: Management plans for athletes with hemophilia must focus on prevention and early intervention.

Cited by 4 publications

References 8 publications

Qualidade de vida de pacientes hemofílicos acompanhados em ambulatório de hematologia

Qualidade de vida de pacientes hemofílicos acompanhados em ambulatório de hematologia

Physical activity and joint function in adults with severe haemophilia on long-term prophylaxis

Physical fitness, functional ability and quality of life in children with severe haemophilia: a pilot study

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