Neurofibromatosis v. Recklinghausen mit intrakranialer Stenose der A. carotis interna bei orbito-sphenoidaler Knochendysplasie

Abstract

A patient with fibromatosis of the skull and a so-called "parophthalmicus syndrome" is described in whom there was hypoplasia and stenosis of the homolateral internal carotid artery and aplasia of the ophthalmic artery. The vascular changes in this phakomatosis are discussed. We suggest that the vascular changes in the carotid be included in the extended parophthalmicus syndrome.