The Anesthetic Implications of a Patient with Farber's Lipogranulomatosis

Anaesthetic management of a child with Farber's lipogranulomatosis posted for exploratory laparotomy

“…Also multiple growths (lipogranulomas) along the airway tract may present with upper airway obstruction, obscure the laryngeal view, bleed or may get dislodged during traumatic intubation and present as foreign body in the trachea which may worsen ventilation and can precipitate any catastrophic event during airway management. [4] Therefore, it is advised to avoid endotracheal intubation in these patients. [5] However, our patient was considered to have a full stomach; most likely with sepsis with the possibility of need for postoperative mechanical ventilation.…”

“…These patients may present with cardiac conduction defects and one must be vigilant and prepared for management of any cardiac arrhythmia. [4] It is safer to use shorter acting drugs which can safely be administered in presence of altered liver and kidney function. [5] Opioids should be used judiciously as there may be respiratory depression in the postoperative period.…”