А case of erythrokeratodermia variabilis (Mendes da Costa type) in a three-year-old child

The article deals with ethiopathogenetic factors of origin of progredient symmetric erythrokeratodermia of Gottron which is mainly characterized by autosomal dominant mode of inheritance and is classified as a disorder of cornification with extra epidermal cellular proliferation.Clinicopathologic criteria on the basis of which this pathology can be verified are described here, such as: onset of a disease at an early age, strictly divided polycyclic, fixed, hyperkeratotic plaques with a narrow erythematic crown and a clean-cut, sometimes hyper pigmented edge, which are symmetrically located on skin on head, buttocks, limbs and are not prone to quick peripheral growth; large frequency of palmoplantar keratoderma and also histological changes typical of erythrokeratodermia.The article describes a rare clinical case of autosomal-recessive progredient symmetric erythrokeratodermia of Gottron which is distinguished by seasonal changes of skin pathological process — emergence of rash in winter and complete remissions in summer.

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Progressive symmetric eritrocarotodermia Gottron: A rare case

Тлиш

Sycheva

Бойко³

et al. 2019

Vestnik dermatologii i venerologii

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А case of erythrokeratodermia variabilis (Mendes da Costa type) in a three-year-old child

Abstract: The authors describe a case of erythrokeratodermia variabilis (Mendes da Costa type) in a three-year-old child. They present data on the clinical picture and histological examination. Major stages of the etiology and pathogenesis of the diseases are described.

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Progressive symmetric eritrocarotodermia Gottron: A rare case

Progressive symmetric eritrocarotodermia Gottron: A rare case

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