Aim. Our study aimed to determine prognostic factors for survival and recurrence in myxofibrosarcomas based on the experience of a single institution. Methods. Patients who had been diagnosed with a myxofibrosarcoma were identified from our database. Survival and recurrence were evaluated with Kaplan Meier survival curves for univariate and cox regression for multivariate analysis. Results. 174 patients with a diagnosis of myxofibrosarcoma were identified. Two patients were excluded due to incomplete information, leaving 172 patients with a mean age of 67 years. Surgery was undertaken in all but 6 patients. Five-year survival was better for myxofibrosarcomas when compared to other soft tissue sarcomas (63% versus 57%). Size, grade of tumour, age, and metastases were all found to be prognostic factors. Local recurrence occurred in 29 patients (17%) with an overall risk of 15% at 5 years. Previous inadvertent excision significantly raised this risk to 45%. Wide surgical margins and depth of tumour, however, had no impact on recurrence. Conclusion. Factors previously identified as prognostic did not demonstrate such a relationship in our study, highlighting the unpredictable nature of myxofibrosarcomas. Future treatment may lie in developing an understanding molecular basis of the tumour and directing therapies accordingly.

We conclude that high negative pressure and deep-suctioning causes RUL collapse in children. Any lobar collapse not only prolongs the child's stay in intensive care, but can be associated with further morbidity which may have a serious implication. By improving suctioning technique this morbidity can be significantly reduced.

prednisolone) and propranolol are commonly prescribed and lesions unresponsive (15% cases) have been treated with antiangiogenic agents such as IFN-alpha, sirolimus, vincristine and cyclophosphamide.Invasive measures like hepatic artery ligation or embolization may be tried in complicated cases. Surgical therapy is recommended for uni-lobe lesions, masses with low potential for regression or in suspected malignancy.In summary, this case always had a poor prognosis as it was multifocal, had intra-hepatic shunting and was complicated by CCF and haemorrhage. Unfortunately TAE wasn't successful on this occasion but sub-speciality involvement was greatly appreciated.

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