No abstract

No abstract

Objective: Congenital heart diseases in childhood are an important cause of morbidity and mortality. The frequency of non-cardiac anomalies in children with congenital heart diseases is between 7-50%. Urinary system anomalies are an important risk factor in children with congenital heart diseases. The aim of this study was to evaluate the presence, types and frequency of urinary system anomalies detected during cardiac catheterization in children with congenital heart diseases. Methods: The cineurography records of 6000 patients who underwent cardiac catheterization due to congenital heart diseases were retrospectively analyzed. Urinary system anomalies detected were examined as renal agenesis, renal ectopia, renal fusion, dysplastic kidney, obstructive uropathy, vesicoureteral reflux, ureter anomaly and bladder anomaly. Patients were grouped as right ventricular outflow tract obstruction, left ventricular outflow tract obstruction, left-to-right shunted hearth disease and, cyanotic or complex heart diseases. The groups were compared in terms of urinary system anomaly types. Results: Seventy-six patients (47 male and 29 female) with urinary system abnormalities were detected. Obstructive uropathy was found in 43 (56.5%) patients, renal agenesis was found in 14 (18.4%) patients, ureter anomaly was found in 14 (18.4%) patients, renal fusion was found in 3 (3.9%) patients, renal ectopia was found 1 (1.3%) patient, vesicoureteral reflux was found in 1 (1.3%) patient. There was no significant difference in term of the urinary system anomaly types among the groups (p>0.05) Conclusion: Urinary system anomalies may also be frequently accompanied in children with congenital heart diseases, so urinary system should also be evaluated during the cardiac catheterization procedure.

Congenital heart disease is the most common congenital condition diagnosed in children and extracardiac abnormalities are frequent among patients with congenital heart disease. Associated urinary tract anomalies in these children are frequently silent, even though potentially significant with a prevalence of 7.5% to 12%.Patients whom were being followed-up and diagnosed with renal anomaly during the procedure of cardiac catheterization in Çukurova University Faculty of Medicine in Balcali Hospital are studied. During cardiac cathetherization renal anomaly was detected in 78 of children with congenital cardiac defects.%28.5 of the detected renal anomalies in patients were bilateral. 29 of the patients detected with renal anomalies were female (%37.7) and 48 of them were male (%62.3). Detected renal anomalies were hydronephrosis in%24.7; pelvicalyceal dilatation in%16.8; hydroureteronephrosis in%15.5; double collecting tubule system in%11.6; renal agenesia in%11.6; bifid pelvis in%7.8; dilatation of renal calyx in%2.5; renal hipoplasia in%2.5 ; horseshoe kidney in%2.5; extra renal pelvis in%1.2; triple renal pelvis in%1.2; ureter dilatation in%1.2; cross ectopic kidney in%2.4; in%1.2 of the patients double calyx are detected.Herein, we emphasised the importance of obtaining abdominal cineradiograph of children in the procedure of cardiac cathetherization for the detection of urinary tract abnormalities.

The incidence of acute postinfectious glomerulonephritis (PIGN) has decreased worldwide, particularly in developed countries. Although PIGN continues to be the most common cause of acute nephritis in children globally, it primarily occurs in developing countries.There is a certain increase in the number of patients with postinfectious glomerulonephritis (PIGN) in Department of Paediatric Nephrology at Cukurova University during November-December 2016. Clinical, laboratory and follow up results of the 13 patients that have PIGN are studied. Paediatricians‘ diagnostic approaches and the reasons for referral were evaluated in patients with clinical symptoms of PIGN. The patients are diagnosed PIGN in the presence of haematuria, proteinuria, evidence of recent streptococcal infection (increase of ASO and throat swab positivity for pharyngitis), low serum C3 levels with normalisation on 8 weeks follow up. 13 patients (5 male, 8 female) are conducted into the study. Mean age was 9 (3-15). All of patients have had recent infection. The symptoms of patients at the time of admission were oedema (70%), macroscopic haematuria (23%), hypertension (15.3%) and respiratory distress (15.3%). 7 of the patients (53%) had blood pressure higher than 95.percetile for age, gender and height. Non nephrotic proteinuria was detected in 11 patients. All patients had low C3 levels. Two of the patients had cardiac systolic dysfunction, pulmonary oedema, and a referral to our hospital. There was improvement in clinical findings with fluid restriction and diuretic therapy in patients‘ follow-ups. Because of nephrotic proteinuria and acute kidney injury, kidney biopsy was done to one of the patients and diagnosed with diffuse proliferative glomerulonephritis.PIGN is observed with higher incidence in the developing countries. In these patients with different clinical presentation, it was aimed to draw attention of paediatricians.