Steatocystoma multiplex is a rare genetic disorder characterized by the presence
of hamartomatous malformations at the junction of the pilosebaceous duct. It
consists of encapsulated cystic lesions in the dermis, with adjacent sebaceous
gland. When associated with inflammation, resembling hidradenitis, it is called
steatocystoma multiplex suppurativa, a condition rarely reported. This is the
first case of steatocystoma multiplex suppurativa reported in the Brazilian
literature. Female patient, 23 years old, with papular and nodular cystic
lesions that started in the armpits and groin, later spreading to the trunk,
lower limbs, anticubital fossa, face and scalp. The presence of papular-nodular
lesions associated with disseminated hidradenitis-like lesions in flexural areas
and the histopathological diagnosis of steatocystoma defined the diagnosis of
steatocystoma multiplex suppurativa.
Pemphigus foliaceus is a chronic autoimmune disease of the skin, clinically
characterized by scaly and crusty cutaneous erosions involving the seborrheic
areas. The patient can eventually become erythrodermic. There are reports of
atypical cases of pemphigus foliaceus with pustules and neutrophils, and
clinical differentiation from generalized pustular psoriasis of von Zumbusch is
difficult. We report the case of a 55-year-old man with a history of psoriasis
vulgaris that has developed pemphigus foliaceus with pustules, triggered by
withdrawal of systemic corticosteroids. This is the first report associating
this atypical form of pemphigus with psoriasis, suggesting that an overlap with
generalized pustular psoriasis can occur.
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