Steatocystoma multiplex is a rare genetic disorder characterized by the presence
of hamartomatous malformations at the junction of the pilosebaceous duct. It
consists of encapsulated cystic lesions in the dermis, with adjacent sebaceous
gland. When associated with inflammation, resembling hidradenitis, it is called
steatocystoma multiplex suppurativa, a condition rarely reported. This is the
first case of steatocystoma multiplex suppurativa reported in the Brazilian
literature. Female patient, 23 years old, with papular and nodular cystic
lesions that started in the armpits and groin, later spreading to the trunk,
lower limbs, anticubital fossa, face and scalp. The presence of papular-nodular
lesions associated with disseminated hidradenitis-like lesions in flexural areas
and the histopathological diagnosis of steatocystoma defined the diagnosis of
steatocystoma multiplex suppurativa.
Dermatofibroma is a benign fibrohistiocytic tumor, common and easily diagnosed when
classical clinicopathologic features are present. The atrophic variant of
dermatofibroma is of uncertain origin. This lesion is characterized clinically by a
flat or atrophic and depressible surface. Histopathological features show reduction
of the thickness of the dermis and elastic fibers. We report a typical case of this
uncommon and probably underdiagnosed variant.
Morbihan disease is a rare condition characterized by chronic and persistent
erythematous solid edema localized on the face. It is believed to be a
complication of rosacea and may occur at any stage of the disease. Features of
this condition include variable therapeutic response and great refractoriness.
We report a case of a 61-year-old man with rosacea history diagnosed with
Morbihan disease, who showed excellent therapeutic response with the combination
of deflazacort and oral isotretinoin but developed recurrence after
corticosteroid discontinuation. We believe that in severe cases of lymphedema of
the face this combination is effective and corticosteroid suspension should be
done slowly and gradually.
Blue nevi are benign melanocytic lesions located in the deeper reticular dermis,
consequence of failure of melanocytic migration into the dermal-epidermal
junction from the neural crest. Lesions are usually asymptomatic and solitary,
but may present in a multiple or agminated (grouped) pattern. The agminated
subtype is formed when bluish-pigmented lesions cluster together in a
well-defined area. Lesions can be flat or raised. We report the case of a
patient who presented multiple bluish macules (1-3 mm in diameter) grouped on
the left upper back. Dermoscopy and anatomic pathological examination were
consistent with blue nevus.
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