Microangiopathy of the brain and retina (Susac's syndrome)

Treatment of Susac's syndrome

“…At least 11 reports on SS have included brain biopsy results [1,5,[6][7][8][9][10][11][12][13][14]. Most have described small foci of necrosis (microinfarcts) within the cerebral cortex and white matter, with loss of neurons, axons, and myelin.…”

Susac's syndrome: A case of simultaneous development of all three components of the triad

“…Since the disease has nonspecific clinical manifestations, diagnosis is difficult and often delayed [2][3][4][5][6][7][8][9]. The clinical patterns are variable such as headache, dementia, hemiplegia, seizures, cranial palsies, hearing loss, vertigo, tinnitus and diminution or loss of vision [10][11][12].…”

Susac's Syndrome: Beneficial Effects of Corticosteroid Therapy in a Japanese Case.

“…From an epidemiological aspect, this syndrome is a very rare disorder (1), with all previously reported cases being Caucasians (1)(2)(3)(4)(5)(6)(7)(8)(9)(10)(11)(12)(13)(14)(15)(16)(17)(18)(19). A recent review (16), however, indicates that this syndromeis more common than previously thought.…”