Pregnancy outcome in a woman with prune belly syndrome

Abstract

SummaryPrune belly syndrome is a rare congenital syndrome that primarily affects male fetuses. Affected men are universally infertile; however, there is a paucity of information published on the reproductive potential of affected women. Pregnancy outcomes in affected women have not been described in the literature. We describe the case of pregnancy in an affected woman. Her pregnancy progressed without complication. Her fetus had no stigmata of the syndrome. Her labour and delivery were, however, complicated by a prolonged second stage of labour and need for vacuum-assisted vaginal delivery. BACKGROUND

First Case of Female Prune Belly Syndrome Following In Vitro Fertilization-Induced Pregnancy: A Rare Case Report and Systematic Review of the Literature

“…This is primarily related to the degree of pulmonary hypoplasia, comorbid conditions, and prematurity [1]. Four patients died within the rst day [5,6,10,26] and 7 patients in the rst month [5,6,8,10,13,18,26]; however, our patient and 8 other patients were alive at the time of reporting [12,13,16,17,19,[21][22][23]. To our knowledge, this is the rst case of PBS in a female patient after IVF…”

Pregnant patient with prune belly syndrome: case report

“…(2) Since the disease is very rare, this is the second case of a pregnant woman with prune belly syndrome in the medical literature. (2) ❚ CASE REPORT A 25-year-old primigravida with prune belly syndrome started prenatal care at 12 weeks. At the beginning of pregnancy, the patient weight was 33kg and height of 1.47m.…”

“…(1) Prune belly syndrome affects approximately one in 40 thousand live births, with approximately 95% of cases occurring in males and with male infertility. (2) In women, the syndrome has variable presentations, but fertility is preserved. (2) Since the disease is very rare, this is the second case of a pregnant woman with prune belly syndrome in the medical literature.…”

“…(2) In women, the syndrome has variable presentations, but fertility is preserved. (2) Since the disease is very rare, this is the second case of a pregnant woman with prune belly syndrome in the medical literature. (2) ❚ CASE REPORT A 25-year-old primigravida with prune belly syndrome started prenatal care at 12 weeks.…”