Unilateral pigmented purpuric eruption

Abstract

Three cases of unilateral pigmented purpuric eruption (UPPE) occurring in children aged between 7 and 12 years are reported. The lesions were asymptomatic and occurred on the lower limb and torso; one case demonstrated a quadrantic configuration with a sharp midline cutoff. The purpuric component resolved spontaneously within 3 months in all cases, while pigmentation showed partial resolution in the two cases followed up for 12 months. Our cases support previous reports of UPPE being a benign self-limiting condition mainly affecting young patients. The cause is unknown.

Atypische klinische Manifestation einer Pigmentpurpura

“…PPD typically occurs on the lower extremities in a symmetrical distribution and often shows a benign and self-limited course. Atypical clinical manifestations such as unilateral, linear, zosteriform and granulomatous PPD, as well as long-persisting lesions have also been described [3,4,5]. Because of the variable clinical spectrum and the similar histopathologic findings, a strict nosological classification is sometimes difficult or even impossible to achieve [1,2,6].…”

Atypical clinical presentation of pigmented purpuric dermatosis

“…PPD typically occurs on the lower extremities in a symmetrical distribution and often shows a benign and self‐limited course. Atypical clinical manifestations such as unilateral, linear, zosteriform and granulomatous PPD, as well as long‐persisting lesions have also been described ‘3, 4, 5’. Because of the variable clinical spectrum and the similar histopathologic findings, a strict nosological classification is sometimes difficult or even impossible to achieve ‘1, 2, 6’.…”

Another, new dermatosis in the spectrum of pigmented purpuric dermatoses or atypical variant of lichen aureus?

“…The traditional classification includes six subtypes: lichen aureus, itching purpura, purpura annularis telangiectodes (Majocchi purpura), pigmented purpuric lichenoid dermatitis of Gougerot-Blum, progressive PPD (Schamberg purpura), and eczematid-like purpura of Doucas and Kapetanakis [1]. Nevertheless, there are some descriptions of cases that share the histopathological features of PPD, but the clinical presentation is not typical for any of the above-mentioned entities [2][3][4]. We describe another atypical case, which is clinically and dermatoscopically similar to the one presented by Zalaudek et al [4].…”

“…Według tradycyjnej klasyfikacji do spektrum PPD zalicza się: liszaja złocistego, plamicę świądową, plamicę obrączkową teleangiektyczną (chorobę Majocchiego), liszajowate plamicze zapalenie skóry (zespół Gougerota-Bluma), postępującą plamicę barwnikową (chorobę Schamberga) i plamicę wypryskopodobną (chorobę Doucasa-Kapetanakisa) [1]. W piśmiennic-twie dostępne są jednak opisy przypadków, w których obraz histologiczny jest charakterystyczny dla PPD, a objawy klinicznie nie odpowiadają żadnej z wymienionych chorób [2][3][4]. Przedstawiamy kolejny, nietypowy przypadek, który jest zbliżony pod względem obrazu klinicznego i demoskopowego do przypadku opisanego w pracy Zalaudek i wsp.…”