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A comprehensive examination and dynamic observation of a patient with clinical manifestations of connective tissue dysplasia and dissection of the internal carotid arteries revealed a symptom complex characteristic of Harlequin syndrome. The description of this form of pathology is given for the first time in the national literature. A brief review presents the diagnostic criteria and mechanisms for the development of this rare autonomic dysfunction.

The article describes the clinical manifestations of dural arteriovenous fistula, which is an abnormal communication between the arteries of the dura mater and venous sinuses or cortical veins. Information on the etiology and pathogenesis of such malformation in domestic literature is limited to a few publications. Diagnosis is based on the identification of visual (pulsation of the earlobe) and acoustic phenomena in the patient, the presence of neuroimaging, in particular MR angiography, a shunt between the posterior auricular artery (branch of the external carotid artery) and the dural venous sinuses. The best treatment method is neurosurgical intervention using endovascular surgery.